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RNA Metabolism Gene Mutation Linked to Rare Disease


RNA Metabolism Gene Mutation Linked to Rare Disease
May 10, 2021
[Source: KTSDESIGN/SCIENCE PHOTO LIBRARY/Getty Images]
Scientists have linked a protein complex, GEMIN5, that controls RNA metabolism in neurons to a rare disease for the first time.  An international group led by researchers at UPMC Children’s Hospital of Pittsburgh found a mutation in this gene is associated with a neurological disorder marked by developmental delay and loss of coordination, or ataxia.
GEMIN5 is one of the key building blocks of a protein complex that controls RNA metabolism in neurons. No mutations in this gene were previously linked to any genetic disease. However, defects in RNA-mediated gene expression control are a hallmark of several human disorders. ....

Deepa Rajan , Udai Pandey , Nature Communications , University Of Pittsburgh School Medicine , Pitt School Of Medicine , Pittsburgh School , Pitt School , Neurogenetics Clinic , இயற்கை தகவல்தொடர்புகள் , பல்கலைக்கழகம் ஆஃப் பிட்ஸ்பர்க் பள்ளி மருந்து , குழி பள்ளி ஆஃப் மருந்து , பிட்ஸ்பர்க் பள்ளி , குழி பள்ளி ,

Mutations Cause Rare Genetic Disease in Children


Date Time
Mutations Cause Rare Genetic Disease in Children
In a paper published today in Nature Communications, an international group of collaborators led by researchers at UPMC Children’s Hospital of Pittsburgh have identified a genetic cause of a rare neurological disorder marked by developmental delay and loss of coordination, or ataxia.
The disorder, scientists found, is caused by mutations in a protein called GEMIN5 one of the key building blocks of a protein complex that controls RNA metabolism in neurons. No mutations in GEMIN5 were previously linked to any genetic disease.
“It’s just like building a house,” said senior author Udai Pandey, Ph.D., associate professor of pediatrics, human genetics and neurology at the University of Pittsburgh School of Medicine. “You take out the most important brick at the base and the whole building falls apart.” ....

Sukhleen Kour , Eric Anderson , Tyler Fortuna , Deepa Rajan , Udai Pandey , Dhivyaa Rajasundaram , Nature Communications , University Of Pittsburgh Children Neuroscience Institute , University Of Pittsburgh School Medicine , Pitt School Of Medicine , Pittsburgh School , Pitt School , Neurogenetics Clinic , Caroline Ward , Pittsburgh Children , Neuroscience Institute , எரிக் ஆண்டர்சன் , இயற்கை தகவல்தொடர்புகள் , பல்கலைக்கழகம் ஆஃப் பிட்ஸ்பர்க் பள்ளி மருந்து , குழி பள்ளி ஆஃப் மருந்து , பிட்ஸ்பர்க் பள்ளி , குழி பள்ளி , கரோலின் வார்டு , பிட்ஸ்பர்க் குழந்தைகள் , நரம்பியல் நிறுவனம் ,

Researchers find rare genetic disease caused by mutations in protein that controls RNA metabolism


Researchers find rare genetic disease caused by mutations in protein that controls RNA metabolism
ANI |
Updated: May 07, 2021 16:55 IST
Pittsburgh [US], May 7 (ANI): An international group of collaborators led by researchers at UPMC Children s Hospital of Pittsburgh have identified a genetic cause of a rare neurological disorder marked by developmental delay and loss of coordination, or ataxia. The research was published in the scientific journal Nature Communications.
The disorder, scientists found, is caused by mutations in a protein called GEMIN5 one of the key building blocks of a protein complex that controls RNA metabolism in neurons. No mutations in GEMIN5 were previously linked to any genetic disease. ....

Deepa Rajan , Udai Pandey , Nature Communications , University Of Pittsburgh School Medicine , Pitt School Of Medicine , Pittsburgh School , Pitt School , Neurogenetics Clinic , இயற்கை தகவல்தொடர்புகள் , பல்கலைக்கழகம் ஆஃப் பிட்ஸ்பர்க் பள்ளி மருந்து , குழி பள்ளி ஆஃப் மருந்து , பிட்ஸ்பர்க் பள்ளி , குழி பள்ளி ,